Synovial Sarcoma of the Vulva: A Rare Yet Existing Entity! Case Report

Alimi Amal*, Khlifi Abdeljalil, Kouira Mouna, Bannour Imene, Hidar Samir, Bibi Mohamed and Khairi Hedi

Université de Sousse, Faculté de Médecine de Sousse, Hôpital Farhat Hached, Service de Gynécologie Obstétrique, Tunisie

^*Correspondance to: Alimi Amal 

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Abstract:

Vulvar cancer is the fifth gynecological cancer after that of the breast, cervix, uterus, and ovaries. The most common histological type is epidermoid carcinoma. But, the vulva, defined histologically by the set of several tissues (cutaneous, glandular, adipocytes, muscular, mucous) can undergo several modifications resulting in lesions of multiple histological nature that might be rare like the synovial sarcoma of the vulva. Few cases have been reported in the literature. Despite this terminology, the Synovial Sarcoma (SS) is not synovial origin, but is derived from multipotent stem cells capable of differentiating into mesenchymal and epithelial cells. The median age at diagnosis is 50 years old, and the most common symptom is a local discomfort or pain during sex. These lesions are often wrongly diagnosed as cysts or Bartholin abscess. The therapeutic management of synovial sarcoma is primarily surgical with wider excision of the lesion with healthy tissue margins. The prognosis is poor. The average rate of locoregional recurrence or metastasis of SS at two years is 50%. The most frequent metastatic sites are the regional lymph nodes, lung, bone and liver. We report the case of a 40-year-old woman with synovial sarcoma of the vulva. The management of this tumor requires multidisciplinary approach.

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Cite the Article:

Amal A, Abdeljalil K, Kouiramouna, Imene B, Samir H, Mohamed B, et al. Synovial Sarcoma of the Vulva: A Rare Yet Existing Entity! Case Report. Ann Clin Case Rep. 2021; 6: 2059..