A Case of Antiphospholipid Syndrome (APS)-Chronic Thromboembolic Pulmonary Hypertension (CTEPH)

Zhao Jiu Liang, Li Can, Wang Qian, Zhao Yan, He Kun, Wu Yan and Liu Sheng

Department of Rheumatology, Peking Union Medical College Hospital, China
Department of Medicine, Peking Union Medical College Hospital, China
Department of Cardiology, Fu Wai Hospital, Chinese Academy of Medical Science, China
Department of Cardiac Surgery, Fu Wai Hospital, Chinese Academy of Medical Science, China

^*Correspondance to: Zhao Jiu Liang 

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Abstract:

Chronic Thromboembolic Pulmonary Hypertension (CTEPH) is the group 4 pulmonary hypertension, related to blood clots blocking the arteries of the lung. CTEPH can be a complication of APS. Patient with CTEPH can develop varies symptoms, which are not specific. So the diagnosis of CTEPH is difficult. Once CTEPH diagnosed, anticoagulation should be used for the patient. Pulmonary thromboendarterectomy (PTE) is the optimal therapeutic schedule for CTEPH now. Hereby we present a case of a CTEPH patient with APS. From this case, we found that when acute PE appeared on an APS patient, CTEPH should be considered. We also found that PTE is effective on CTEPH developed from APS.

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Cite the Article:

Liang ZJ, Can L, Qian W, Yan Z, Kun H, Yan W, et al. A Case of Antiphospholipid Syndrome (APS)- Chronic Thromboembolic Pulmonary Hypertension (CTEPH). Ann Clin Case Rep. 2017; 2: 1481.